Behavioral and psychiatric problems
- Behavioral and psychiatric problems may interfere with quality of life for adolescents and in adulthood.
- These behaviors can be persistent. They may escalate in severity and intensity with age (particularly from adolescent to adulthood).
- This escalation is independent of intellectual, language, and motor abilities.
Characteristic behavior profile
- People with PWS have a characteristic behavior profile which includes: temper tantrums, stubbornness, emotional lability, exaggerated emotional response, controlling and manipulative behaviors, compulsivity, and difficulty with changes in routine.
- Many behavioral challenges are similar to those found in people diagnosed with autism or autism spectrum disorders.
- Attention Deficit Hyperactivity Disorder (ADHD) may be seen.
- Perseveration and repetitive behaviors are common.
- Students with PWS can be demanding and prone to rage episodes when frustrated.
- Psychosis is reported in young adulthood in 10-20% of people who have PWS.
- By late adolescence, about 15% will have a diagnosed mood disorder.
- Delusions and paranoid ideation are more common in people with PWS than in the general population.
- They may have obsessive compulsive tendencies:
- These behaviors can be a source of strain in families, and in living and work environments.
- The constant need to monitor food intake can be very stressful for families.
- This is due to an abnormally increased appetite and the eating of unusual food related items (i.e. sticks of butter, used cooking grease, decaying food, garbage, and food flavored items like shampoo).
- Hoarding food when it is accessible is common.
Judgment about social cues
- Social judgment can be poor. Interpretations of social information by students with PWS are similar to some children who have a pervasive development delay.
- They may have an inability to read other’s facial expressions, decode emotion, and have difficulty interpreting visually presented social information.
- decreased sensitivity to pain
- a tendency to not run a fever even when significantly ill
- increased skin picking and picking at other body areas